초록접수 현황
| 20F-184 | 구연 발표 |
Surgical outcomes of primary supravalvar aortic stenosis repair
Eun Seok Choi, Chun Soo Park, Bo Sang Kwon, Tae-Jin Yun
Divisions of Pediatric Cardiac Surgery, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Korea
Purpose : Supravalvar aortic stenosis (SVAS) is a rare congenital anomaly. The aim of the study was to review outcomes of patients who underwent repair of SVAS at a single institution.
Methods : Between 1999 and 2018, 39 patients underwent surgical repair of primary SVAS. A total of 26 patients had Williams syndrome. Median age at operation was 4.3 years (range, 0.3 to 25.6 years), and median weight at operation was 16.9 kg (range, 5.9 to 55.0 kg). The surgical technique of modified simple sliding aortoplasty was applied in 35 (89.7%) patients. Pulmonary artery stenosis was repaired concomitantly in 13 (33.3%) patients. Medical records were reviewed retrospectively.
Results : The median follow-up time 8.9 years (range 1.7 – 20.7 years). Survival rates at 5, 10 years were 96.8%. Freedom from left ventricular outflow tract reoperation at 5, 10, 16 years were 91.7%, 91.7%, and 68.8%, respectively. Freedom from all-cause reoperation at 5, 11, 16 years were 86.3%, 79.1%, and 59.3%, respectively. Age younger than 2 years (HR, 6.99. 95% CI, 1.20-40.69, p = 0.031) was a risk factor for all-cause reoperation in Cox regression analysis.
Conclusion : Long term survival was excellent in patients with surgical repair of SVAS. But all-cause reoperation rate was relatively high. Age younger than 2 years was a predictor of all-cause reoperation.
Methods : Between 1999 and 2018, 39 patients underwent surgical repair of primary SVAS. A total of 26 patients had Williams syndrome. Median age at operation was 4.3 years (range, 0.3 to 25.6 years), and median weight at operation was 16.9 kg (range, 5.9 to 55.0 kg). The surgical technique of modified simple sliding aortoplasty was applied in 35 (89.7%) patients. Pulmonary artery stenosis was repaired concomitantly in 13 (33.3%) patients. Medical records were reviewed retrospectively.
Results : The median follow-up time 8.9 years (range 1.7 – 20.7 years). Survival rates at 5, 10 years were 96.8%. Freedom from left ventricular outflow tract reoperation at 5, 10, 16 years were 91.7%, 91.7%, and 68.8%, respectively. Freedom from all-cause reoperation at 5, 11, 16 years were 86.3%, 79.1%, and 59.3%, respectively. Age younger than 2 years (HR, 6.99. 95% CI, 1.20-40.69, p = 0.031) was a risk factor for all-cause reoperation in Cox regression analysis.
Conclusion : Long term survival was excellent in patients with surgical repair of SVAS. But all-cause reoperation rate was relatively high. Age younger than 2 years was a predictor of all-cause reoperation.
첨부파일 : 대흉 초록 SVAS.pptx
책임저자: Chun Soo Park
Divisions of Pediatric Cardiac Surgery, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Korea
발표자: Eun Seok Choi, E-mail : gninihs@naver.com