Recurrent Primitive Neuroectodermal Tumor in the Chest Wall 16 Years after First Operation

Young Sam kim, Joung Teak Kim, Wan ki Baek, Yong Han Yoon

Department of Thoracic and Cardiovascular Surgery, Inha University Hospital, Inha University College of Medicine, Incheon, Korea

Background : Primitive neuroectodermal tumor of the chest wall is a rare malignant tumor that is second most common sarcoma in children and young adults, and is associated with poor survival despite multimodality treatment regimens.

Methods : A 17-year old woman was admitted with moderate early morning chest pain. The chest mass wall was resected with partial of the 7th and 8th ribs and intercostal muscle, parietal pleural and wedge resection of RUL, RLL were performed and the chest wall was reconstructed. Microscopic pathologic findings revealed recurrent primitive neuroectodermal tumor that involved vascular structures and invaded bone.

Results : The patient experienced no recurrence during the 4 years following wide chest wall resection, reconstruction, and intensive chemoradiation therapy.

Conclusion : Primitive neuroectodermal tumor of the chest wall is a rare and the prognosis is poor. We report a case of recurrent PNET of the chest wall with an onset 16 years after initial surgery that was treated by wide surgical excision and chemoradiotherapy.

책임저자: Yong Han Yoon

Department of Thoracic and Cardiovascular Surgery, Inha University Hospital, Inha University College of Medicine, Incheon, Korea

발표자: Yong Han Yoon, E-mail : yoonkwon@inha.ac.kr