Long Term Surgical Outcomes of Fibromatosis in Thorax
서동주, 황수경, 문덕환, 주석, 이근동, 최세훈, 김형렬, 김용희, 김동관, 박승일
울산대학교 의과대학 서울아산병원 흉부외과학교실
Background : The term fibromatosis refers to a group of benign soft tissue tumors which have certain characteristics in common, including absence of cytologic and clinical malignant features, histology consistent with proliferation of well-differentiated fibroblasts, an infiltrative growth pattern, and aggressive clinical behavior with frequent local recurrence. The preffered treatment option is surgical resection. However, the surgical outcome of thoracic fibromatosis has not been elucidated. In this study, we sought to evaluate long term results of the resection of thoracic fibromatosis outcomes.
Methods : From January 2001 to June 2014, a total of 29 patients (aged 41.3 ± 13.7 years, 14 females) who underwent resection of thoracic fibromatosis were reviewed, retrospectively. We analyzed the relationships between genders, age, recurrences, and mortality.
Results : Wide surgical excision was performed in all patients, which had clear resection margin. The tumors were located in the chest wall side of ribs and infraclavicular region in 10 patients, in the mammary and axillary intramuscular region in 9 patients each, and in the intrathoracic and paravertebral region in 10 patients. The median follow up period was 102.5 ± 102.2 months (range, 5.92-383.7 months). There was no in-hospital mortality, and only one patient died due to other disease during the follow up period. Local recurrence developed in nine (31%) patients. Six (66.7%) patients of them recurred only once, and three (33.3%) patients recurred more than once. The median period until recurrence after initial operation was 18.72 ± 8.64 months (range, 8-36 months). All recurred tumor was resected again; since then there was no recurrence.
Conclusion : The surgical resection may be a treatment of choice in patients with thoracic fibromatosis. Because of the good postoperative outcomes, surgical resection is recommended in the patient with recurred tumor.
책임저자: 김동관
울산대학교 의과대학 서울아산병원 흉부외과학교실
연락처 : 서동주, Tel: 02-3010-3580 , E-mail : na2336@naver.com